COG8 polyclonal antibody
产品名称： COG8 polyclonal antibody
英文名称： COG8 polyclonal antibody
产品编号： PAB15620
产品价格： null
产品产地： 台湾
品牌商标： Abnova
更新时间： null
使用范围：
亚诺法生技股份有限公司（Abnova)
- 联系人 :
- 地址 : 台湾台北市内湖区洲子街 108 号 9 楼
- 邮编 : 11493
- 所在区域 : 台湾
- 电话 : +886-920**1152 点击查看
- 传真 : 点击查看
- 邮箱 : sales@abnova.com.tw
- Specification
- Product Description:
- Goat polyclonal antibody raised aganist synthetic peptide of COG8.
- Immunogen:
- A synthetic peptide corresponding to amino acids at internal region of human COG8.
- Sequence:
- C-KAIQETVEKFQEE
- Host:
- Goat
- Theoretical MW (kDa):
- 68.4
- Form:
- Liquid
- Purification:
- Antigen affinity purification
- Concentration:
- 0.5 mg/mL
- Storage Buffer:
- In Tris saline, pH 7.3 (0.5% BSA, 0.02% sodium azide)
- Storage Instruction:
- Store at -20°C.
Aliquot to avoid repeated freezing and thawing.
- Recommend Usage:
- ELISA (1:16000)
The optimal working dilution should be determined by the end user.
- Note:
- This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Publication Reference
- 1.
- A new inborn error of glycosylation due to a Cog8 deficiency reveals a critical role for the Cog1-Cog8 interaction in COG complex formation.
Foulquier F, Ungar D, Reynders E, Zeevaert R, Mills P, Garcia-Silva MT, Briones P, Winchester B, Morelle W, Krieger M, Annaert W, Matthijs G.Hum Mol Genet. 2007 Apr 1;16(7):717-30. Epub 2007 Jan 12.
- Application Image
- ELISA
- Entrez GeneID:
- 84342
- Protein Accession#:
- NP_115758.3
- Gene Name:
- COG8
- Gene Alias:
- DOR1,FLJ22315
- Gene Description:
- component of oligomeric golgi complex 8
- Gene Ontology:
- Hyperlink
- Gene Summary:
- This gene encodes a protein that is a component of the conserved oligomeric Golgi (COG) complex, a multiprotein complex that plays a structural role in the Golgi apparatus, and is involved in intracellular membrane trafficking and glycoprotein modification. Mutations in this gene cause congenital disorder of glycosylation, type IIh, a disease that is characterized by under-glycosylated serum proteins, and whose symptoms include severe psychomotor retardation, failure to thrive, seizures, and dairy and wheat product intolerance. [provided by RefSeq
- Other Designations:
- conserved oligomeric golgi complex component 8,dependent on RIC1